오른쪽 발등에 발생한 선단혈관피부염 1예

Abstract

Acroangiodermatitis (AAD) is a rare reactive vasculo-proliferative disorder associated with chronic venous hypertension. Owing to its clinical and histological similarities to Kaposi sarcoma, AAD is also known as pseudo-Kaposi sarcoma. AAD is characterized by several clearly defined red-purple papules, plaques or ulcerations located on the dorsum of the foot and medial lower limbs. We describe the case of a 36-year-old woman who had multiple red-purple papules and plaques on the dorsum of the right foot area. A skin biopsy was performed, and histopathological examination revealed the presence of multiple capillaries lined by a single layer of endothelial cells surrounded by hemosiderin deposits. No specific histological features of Kaposi sarcoma were observed. Immunohistochemical analysis showed CD31＋ positivity in endothelial cells. The patient was diagnosed with AAD and the lesions have shown no remission for the past 7 years. Therefore, follow-up biopsies are performed every 2 or 3 years to monitor for any potential malignant changes.