Malignant Peripheral Nerve Sheath Tumor in Frontal Sinus, Orbital Cavity and Ethmoid Cavity

Abstract

Malignant peripheral nerve sheath tumors are extremely rare soft tissue sarcomas. Among various locations, the trunk and extremities are the most commonly involvedsites, with only 15% of such lesions occuring in head and neck region. Here, we reporta case of a 74-year-old male who presented with forehead swelling and right eyedeviation. Computed tomography images revealed a tumor involving the frontal sinus,ethmoid sinus, and the orbital cavity. The patient underwent a surgical excision of thelesion, which histopathological examination revealed to be a malignant peripheralnerve sheath tumor.